DIAGNOSIS	PFAPA	FMF	HIDS	TRAPS	CINCA/NOMID
Age of Onset	< 5y	< 20y	< 1y	< 65y	< 3mo
Intervals between attacks	Regular	Irregular	Irregular	Irregular	Irregular
Duration of attacks	4 days	1 – 3 days	3 – 7 days	Often>1 week	Variable
Clinical features	Lymphadenopathy pharyngitis oral ulcers	Painful serositis erysiplas – like rash Scrotal involvement	Cervical adenopathy abdominal pain diarrhea/vomiting arthralgia, rash	Periorbital edema Conjunctivitis Localized myalgia Tender erythema	Urticarial rash Deforming arthropathy Chronic meningitis Uveitis Hearing Loss
Ancestry	Many	Mediterranean	Dutch/French	Many	Many
Gene	None	Autosomal recessive MEFV	Autosomal recessive mevonalate kinase		Autosomal dominant CIAS1